Peliosis hepatis associated with hereditary haemorrhagic telangiectasia
نویسندگان
چکیده
Hereditary haemorrhagic telangiectasia (HHT) is an autosomal, predominantly inherited disease characterized by diffuse telangiectases involving the skin, mucous membranes, lung, brain, gastrointestinal tract and liver. Peliosis hepatis is a rare, benign disorder causing sinusoidal dilatation and the presence of multiple blood-filled lacunar spaces within the liver. We report a case of an HHT patient with incidental magnetic resonance findings of focal hepatic peliosis.
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1. Kim EA, Yoon KH, Jeon SJ, Cai QY, Lee YW, Yoon SE, et al. Peliosis hepatis with hemorrhagic necrosis and rupture: a case report with emphasis on the multi-detector CT findings. Korean J Radiol. 2007;8:64–9. 2. Wang SY, Ruggles S, Vade A, Newman BM, Borge MA. Hepatic rupture caused by peliosis hepatis. J Pediatr Surg. 2001;36:1456–9. 3. Cereceda N, Solı́s Herruzo J, Muñoz-Yagüe M, de Blas C. P...
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